9. Creutzfeldt-Jakob Disease (Cjd). It Is A Rare,...

9. Creutzfeldt-Jakob disease (CJD) It is a rare, degenerative but fatal brain disorder affecting very a small fraction of persons. The symptoms usually arise at the age of 60 and the person dies within a year. Many researchers believe that this disorder is the result of an abnormal protein known as prion. About 5-10% cases reported in the United States share a genetic basis where this form of dementia is caused by a mutation in the gene for the prion protein. Patients with Creutzfeldt-Jakob disease suffer from the problems associated with muscle coordination, personality changes, impaired memory, judgment making, thinking disability and impaired vision. Other possible symptoms include insomnia and depression. In later stages the persons†¦show more content†¦Some disorders unique to children may also cause dementia. Niemann-Pick disease is a type of inherited disorder where specific gene mutations affect metabolism of cholesterol and lipids so excessive amount of cholesterol accumulates in liver and spleen whi le excessive lipids accumulate in brain. The symptoms include dementia, confusions and problems of learning and memory. The disease is known to affect the young school going children but may also affect teen agers. Batten disease is also a fatal hereditary disorder of the central nervous system occurring in childhood. The symptoms include formation of lipopigments in body tissues and early symptoms include personality and behavior changes, clumsiness or stumbling. As the disease advances children may experience mental impairment, loss of sight and motor skills, become blind and bedridden. Lafora body disease is a rare genetic disorder responsible for causing progressive dementia and movement problems. The symptoms arise in the early childhood or late teens and are characterized by the presence of Lafora bodies in brain, skin, muscles and liver and death of child within 2-10 years. Other conditions causing dementia Doctors have found many conditions that can cause dementia and some symptoms can be reversed with proper treatment. For example, medications can sometimes cause symptoms of dementia. They can be caused either by aShow MoreRelatedTypes Of Dementia For Cerebral Autosomal Dominant Ateriopathy1786 Words   |  8 PagesOther type of dementia can be coupled with a rare hereditary disorder known as CADASIL which stands for cerebral autosomal dominant ateriopathy with subcortical infarct and leukoencephalopathy. This disorder is linked to abnormalities of a specific gene, Notch3 located on chromosome 19. The first symptoms arise at the age of 20 or 35 or 40 and the individuals often die at the age of 65. Researchers are still working to find out the exact cause of CADASIL. Other causes of vascular dementia includeRead Moredementia unit 33 Essay5508 Words   |  23 PagesThere are many diseases that result in dementia. The most common types of dementia are Alzheimer’s disease; vascul ar dementia; Pick’s disease; dementia with Lewy bodies (Fronto-Temporal); Creutzfeldt-Jakob Disease (CJD); Huntington’s disease. Alzheimers disease is one of the most common causes of dementia. The term dementia describes a set of symptoms, which can include memory loss, changes in mood and problems with communication and reasoning. These symptoms occur when certain diseases and conditions